Myoma of the rudimentary uterus in Mayer –Rokitansky – Kuster – Hauser syndrome. Clinical case
نویسندگان
چکیده
The article presents a clinical case of large fibroids with complete aplasia the uterus and vagina (Mayer Rokitansky Kuster Hauser syndrome), retrospective analysis patients anamnestic data, result surgical treatment.
منابع مشابه
Mayer-Rokitansky-Kuster-Hauser Syndrome.
Mayer-Rokitansky-Küster-Hauser Syndrome is a congenital malformation in which there is failure of the Müllerian ducts to develop resulting in absent uterus and fallopian tubes and variable malformations of the vagina. Ultrasonography reveals absence of uterus with normally visualised ovaries.
متن کاملMayer-Rokitansky-Kuster-Hauser syndrome: a review
The congenital aplasia or severe hypoplasia of mullerian structures is infrequent. However, the features of normal female endocrine function paired with the absence of a functional uterus and vagina makes it a fascinating entity. The diagnosis and work-up in these patients has become very efficient, thanks to the use of imaging, and there are multiple successful procedures for the creation of a...
متن کاملColovaginoplasty in a Case of Mayer-Rokitansky-Kuster-Hauser Syndrome
Mayer-Rokitansky-Kuster-Hauser Syndrome (MRKHS) is characterized by various abnormalities of paramesonephric duct structures; vaginal aplasia being the commonest anomaly in the spectrum. We report a 17-year-old girl; a case of MRKHS with vaginal agenesis. The cervix was present but atretic; uterus, fallopian tubes and ovaries were normal. There were no associated renal or skeletal defects. Colo...
متن کاملMayer-Rokitansky-Kuster-Hauser syndrome: recent clinical and genetic findings.
Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is characterized by Mullerian duct aplasia in an XX individual with female phenotype presenting primary amenorrhea at adolescence. Multiple abnormalities may be associated with the MRKH syndrome. Genetic investigations focused on the genes of anti-Mullerian hormone and its receptor, as well as on Wt1, Pax2, Cftr and Hox genes, have been unproductiv...
متن کاملMRI in the diagnosis of Mayer-Rokitansky-Kuster-Hauser syndrome.
PURPOSE The aim of this study was to establish the role of magnetic resonance imaging (MRI) in patients with Mayer-Rokitansky-Kuster-Hauser syndrome (MRKHS). MATERIALS AND METHODS Sixteen female MRKHS patients (mean age, 19.4 years; range, 11-39 years) were studied using MRI. Two experienced radiologists evaluated all the images in consensus to assess the presence or absence of the ovaries, u...
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ژورنال
عنوان ژورنال: Vestnik Volgogradskogo gosudarstvennogo medicinskogo universiteta
سال: 2023
ISSN: ['1994-9499', '1994-9480']
DOI: https://doi.org/10.19163/1994-9480-2023-20-1-171-175